Retinitis Pigmentosa
 
What is retinitis pigmentosa?
Retinitis pigmentosa is actually the name
given to a group of hereditary eye disorders, all of which involve the eye's retina, the
light-sensitive nerve layer that lines the back of the eye, and all of which cause a
gradual, yet progressive, loss or reduction in visual ability.
What causes retinitis pigmentosa?
Retinitis pigmentosa is caused by a variety of different inherited retinal defects -- all
of which affect the ability of the retina to sense light. The retinal defect may be found
in the retina's rod cells (a type of retinal cell found outside of the central portion of
the retina that help to transmit dim light and allow for peripheral vision), the retina's
cone cells (a type of retinal cell found inside the center of the retina that help to
transmit the color and detail of images), and/or in the connection between the cells that
compose the retina.
What are the symptoms of retinitis
pigmentosa?
The following are the most common symptoms of retinitis pigmentosa. However,
each individual may experience symptoms differently, especially with severity and
progression as the most obvious variables. Some persons with retinitis pigmentosa
experience a slow, very progressive loss of vision, while others lose their visual ability
much more quickly and severely. Other common symptoms may include:
- difficulty seeing in poor light (i.e., at dusk or in a dimly lit area) or in the dark
- a diminished visual field, either central vision (a condition called macular dystrophy)
or peripheral vision (sometimes referred to as tunnel vision)
- difficulty reading print (with a loss of central vision)
- difficulty deciphering detailed images (with a loss of central vision)
- difficulty with stumbling or tripping over objects not seen; clumsiness (with a loss of
peripheral vision)
The symptoms of retinitis pigmentosa may resemble other eye diseases. Consult a
physician for diagnosis.
How is retinitis pigmentosa
diagnosed?
In addition to a complete
medical history and eye examination, your eye care professional may perform one or more of
the following tests to determine how much of the retina is diseased:
- visual acuity test -
the common eye chart test (see right), which measures vision
ability at various distances.
- ophthalmoscopy - a physician performs a detailed examination of the
retina using a special magnifying glass.
- color defectiveness determination test
Treatment for retinitis pigmentosa:
Specific treatment will be determined by your physician(s) based on:
- your age, overall health, and medical history
- extent of the disease
- your tolerance for specific medications, procedures, or therapies
- expectations for the course of the disease
- your opinion or preference
Unfortunately, to date, there is no specific treatment for retinitis pigmentosa.
However, protecting the eye's retina with the use of UV sunglasses may be helpful in
delaying the onset of symptoms. Consult your physician for more information.
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